Peter van Mourik

219 List of abbreviations KUL - Katholieke Universiteit Leuven LIS - LIS µ-/m-/ l - micro-/ milli-/ liter µ-/m-/M - micro-/ milli-/ molar Nac - N-acetylcysteine NCM - Noggin conditioned medium NPD - Nasal Potential Difference PBS0 - Phosphate Buffered Saline (without magnesium and calcium) ppFEV 1 - Percentage predicted forced expiratory volume in one second RhoKi - Rho- Kinase (ROCK inhibitor) ROC - Receiver operation characteristic R-spo3 - hR-spondin-3 RT - Room temperature SD - Standard deviation SLA - Steady state lumen area SCC - Sweat Chloride Concentration Poly-T - Poly-thymidine PTC - Premature termination codon PTI - Proteostasis Therapeutics UMCU - University Medical Centre Utrecht WCM - Wnt-3A conditioned medium WT - Wild type