Milea Timbergen

165 Table 2. Overview of studies reporting the results of the active surveillance approach in desmoid-type fibromatosis First author, year of publication, inclusion. period Total N FAP/ Gardner N P/R total ASG N P/R ASG Median age ASG Sex M/F ASG Site ASG Median FU (r/ IQR/95% CI) ASG PD SD PR CR NS Shift to AT AT Dalén, 2006 24 NS 8 NS 6/2 a 8 6/2 a 32.5 3/5 5 AW 1 EG 2 TR 4.6 year (r: 0.8-7.5) 2 1 2 3 0 NS NS Bertagnolli, 2008 25 2001-2006 52 21 NS 4 NS NS 4 NS 4 IA NS  0 4 0 0 0 0/4 NA Bonvalot, 2008 12 1988-2003 112 NS 112/0 11 11/0 NS 11 NS 11 NS NS 3 NS NS NS 8 3/11 1 ST 2 ST+SG Nakayama, 2008 26 1992-2003 11 NS 9/2 11 9/2 28 2/9 2 AW 7 EG 2 HN 56 months (r: 16-132) 1 7 3 0 0 3/11 2 SG 1 ST Fiore, 2009 14 1995-2008 142 6 74/68 83 54/29 NS 22/61 33 AW 27 EG 3 HN 6 IA 14 TR NS 29 35 3 NS 16 26/83 10 NS 6 SG 10 ST Barbier, 2010 27 1989-2009 26 0 11/15 26 11/15 34.5 5/21 26 EG 8 months (r: 0-80) 1 24 0 1 0 0/26 NA Salas, 2011 22 1965-2008 426 0 426/0 27 27/0 NS 27 NS 27 NS 52 months (95% CI 43.6- 61.6%) 6 16 5 0 0 NS NS Bonvalot, 2013 10 1993-2012 147 0 147/0 102 102/0 NS 102 NS 102 AW NS NS NS NS NS 102 37/102 15 SG 22 ST Fiore, 2014 2 1985-2011 44 b 0 44/0 27 27/0 NS 0/27 27 NS NS 17 NS NS NS 10 12/44 6 SG 6 ST 6