Suzanne de Bruijn

128 Chapter 3.1 Table S3. Continued Family Subject Age of onset (y) Otoscopic examination Clinical remarks Imaging Audiometry Progression of HL General remarks CT MRI Subject age (y) PTA SRT Maximum SRS (%) Progres- sion rate (dB/y) YOF (y) R L R L R L IV:3 17 N 47 27 25 25 17 100 100 1 34-47 IV:8 27 N 30 38 37 32 30 100 95 2.7 17-30 W04-262 II:11 <18 R atelectasis L sclerotic A, T 70 85 87 >95 >95 37 44 NA 0 Multiple ear surgeries, a.o. ear drum surgery III:4 49 N T 67 40 47 28 35 100 90 NA 0 III:5 55 N NE, T 63 32 23 NT NT NT NT 0.6 49-63 III:8 49 N A 59 43 32 37 22 100 100 1.4 46-59 III:11 32 N A, T N 60 62 55 60 70 95 70 2 47-60 III:14 NOHL N Ab 49 7 7 NT NT NT NT NA NA III:16 25 N A, T 47 70 65 80 77 55 60 0.9 29-47 III:19 28 N A N 49 83 92 NA NA 42 42 2.1 33-49 IV:3 NR N 21 12 7 NT NT NT NT NA 0 W15-0495 II:2 35 NT T 84 73 75 65 70 60 70 0.9 74-84 II:4 PS N 81 77 85 105 105 60 50 2.4 58-81 II:7 60 NT A 80 60 73 55 72 73 55 1.5 70-80 III:3 38 N T, A 55 22 15 19 14 100 97 NA 51-55 III:4 NOHL NT NE 51 8 7 NT NT NT NT NA 0 Noise trauma III:7 50 NT 52 22 20 NT NT NT NT NA 0 III:8 30 N A, T 48 62 58 52 48 92 92 NA 44-51 III:9 43 N NE 46 38 37 42 44 96 90 NA 0 Professional noise exposure