Suzanne de Bruijn

141 A RIPOR2 deletion is a frequent cause of adult-onset hearing loss ! # ! " % % & % % & % % % & ! # ! " % % & % % & ! $ % & % % & ! $ % & ! # ! " % % % & ! $ % & Figure S5. Pure tone audiometry. Air conduction thresholds of all subjects (except III.5 ofW08-1421) with the c.1696_1707del RIPOR2 variant are depicted. In case of symmetry, the averages of left and right ear thresholds are shown. Otherwise, colorized (right red, left blue) audiograms of both ears are depicted. The p95 values are matched to the individuals’ sex and age at the most recent audiometry, according to the ISO 7029:201f7 standard. The age range for which the ISO 7029:2017 can be applied is 18 to 70 years. Part of the pure tone audiometry for family W97-056 has been published previously by Kunst et al. 2000. 18 y, age in years; R, right; L, left; dB HL, decibel hearing level; kHz, kiloHertz; AC; only air conduction levels available, no additional bone conduction thresholds have been measured.