135 Ventriculomegaly and TH | Crouzon Table 1. Patient characteristics Crouzon patients 63 M : F 31 : 32 Age at presentation† 0.7 (0.2 – 2.9) FOHR ≥ 0.4* 31 (18; 13) TH ≥+5mm* 29 (6; 23) FOHR ≥ 0.4 and TH ≥+5mm 18 Lambdoid suture synostosis <1yr of age 12 Head circumference < -1.0 SD 22 Papilledema 33 Moderate/severe OSA 18 Surgeries No surgery 6 Patients that underwent a single surgery 19 Patients that underwent multiple surgeries 38 Types of surgeries Vault expansions‡ 59 (46) Fronto-orbital expansion 15 (Fronto-)biparietal remodellation 20 Occipital expansion classic/spring distraction 24 Midface surgeries‡ 26 (18) Combination vault expansion & midface surgery‡ 25 (22) FM decompressions‡ 3 (3) VP-shunts/ETV and revisions‡ 47 (13) VP-shunt** 8 ETV** 2 VP-shunt + ETV** 3 Endoscopic ventriculostomies‡ 6 (4) Values represent absolute numbers † Median age (interquartile range) in years ‡ Number of surgeries (number of patients) * Values represent number of patients (number of patients in whom event occurred preoperatively; number of patients in whom event occurred postoperatively) ** Values represent absolute number of patients FOHR: fronto-occipital horn ratio, TH: cerebellar tonsillar herniation, OSA: obstructive sleep apnea, FM: foramen magnum, VP-shunt: ventriculoperitoneal shunt, ETV: endoscopic third ventriculostomy 8
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