Mohamed El Sayed

93 ECG changes in Fabry disease P-wave duration in women (ms) Age category Available ECGs in Fabry women, n Fabry women Median (IQR) Available ECGs in Controls- women, n Controls-women Median (IQR) P- value 18-29 28 105 (97-111) 435 104 (96-110) 1.0 30-39 21 108 (102-114) 393 106 (98-112) 1.0 40-49 32 110 (102-120) 463 108 (100-114) 1.0 50-59 32 116 (110-129) 519 112 (104-118) 0.03* 60-69 9 122 (116-128) 399 114 (106-120) 0.1 70+ 1 156 (-) 11 112 (102-121) 0.9 PR-interval in women (ms) Age category Available ECGs in Fabry women, n Fabry women Median (IQR) Available ECGs in Controls- women, n Controls-women Median (IQR) P- value 18-29 28 132 (124-143) 435 146 (134-160) 0.004** 30-39 21 134 (126-162) 393 152 (140-164) 0.1 40-49 32 140 (122-155) 463 152 (140-166) 0.01* 50-59 32 158 (132-177) 519 158 (144-172) 1.0 60-69 9 180 (170-184) 399 158 (146-174) 0.1 70+ 1 244 (-) 11 166 (146-174) 0.9 QRS-duration in women (ms) Age category Available ECGs in Fabry women, n Fabry women Median (IQR) Available ECGs in Controls- women, n Controls-women Median (IQR) P- value 18-29 28 87 (84-94) 435 92 (86-98) 0.06 30-39 21 96 (86-100) 393 90 (86-96) 1.0 40-49 34 97 (88-106) 463 90 (86-97) 0.02* 50-59 38 108 (99-116) 519 92 (86-98) <0.001*** 60-69 16 117 (96-145) 405 92 (86-98) <0.001*** 70+ 4 152 (136-173) 11 90 (85-98) 0.04* QTc in women (ms) Age category Available ECGs in Fabry women, n Fabry women Median (IQR) Available ECGs inControls- women, n Controls-women Median (IQR) P- value 18-29 28 394 (385-413) 435 412 (399-424) <0.001*** 30-39 21 410 (396-423) 393 418 (406-432) 0.2 40-49 34 424 (402-432) 463 421 (409-435) 1.0 50-59 38 429 (417-449) 519 424 (411-437) 0.08 60-69 16 456 (424-485) 405 429 (417-445) 0.1 70+ 4 496 (478-527) 11 428 (419-444) 0.009** 3

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